Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003615228 | SCV004523322 | uncertain significance | Bloom syndrome | 2024-01-03 | criteria provided, single submitter | clinical testing | This sequence change affects a donor splice site in intron 10 of the BLM gene. RNA analysis indicates that disruption of this splice site induces altered splicing and likely results in a shortened protein product. This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with BLM-related conditions. Studies have shown that disruption of this splice site results in skipping of 10 , but is expected to preserve the integrity of the reading-frame (Inviate). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |