Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000672550 | SCV000797663 | likely pathogenic | Bloom syndrome | 2018-02-06 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000672550 | SCV002166617 | pathogenic | Bloom syndrome | 2021-05-07 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has not been reported in the literature in individuals with BLM-related conditions. ClinVar contains an entry for this variant (Variation ID: 556531). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Met1006Aspfs*16) in the BLM gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in BLM are known to be pathogenic (PMID: 17407155). |