Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000709369 | SCV000838981 | uncertain significance | Bloom syndrome | 2018-07-02 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004601260 | SCV005101890 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-04-18 | criteria provided, single submitter | clinical testing | The p.N1022T variant (also known as c.3065A>C), located in coding exon 15 of the BLM gene, results from an A to C substitution at nucleotide position 3065. The asparagine at codon 1022 is replaced by threonine, an amino acid with similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |