Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003506577 | SCV004296602 | pathogenic | Bloom syndrome | 2023-07-28 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Lys272*) in the BLM gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in BLM are known to be pathogenic (PMID: 17407155). This premature translational stop signal has been observed in individual(s) with Bloom syndrome (PMID: 7585968). This variant is also known as A>T at position 888. For these reasons, this variant has been classified as Pathogenic. |