Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000160038 | SCV000210271 | uncertain significance | not provided | 2024-03-08 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Not observed at significant frequency in large population cohorts (gnomAD); Also known as 1732A>C; This variant is associated with the following publications: (PMID: 32377563, 35264596, 29884841, 26997744) |
Ambry Genetics | RCV000223354 | SCV000276062 | likely benign | Hereditary cancer-predisposing syndrome | 2018-03-15 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Labcorp Genetics |
RCV000637723 | SCV000759196 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2023-12-29 | criteria provided, single submitter | clinical testing | This sequence change replaces lysine, which is basic and polar, with glutamine, which is neutral and polar, at codon 502 of the BRCA2 protein (p.Lys502Gln). This variant is present in population databases (rs276174809, gnomAD no frequency). This missense change has been observed in individual(s) with breast cancer (PMID: 10923033, 26997744, 35264596). ClinVar contains an entry for this variant (Variation ID: 125946). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt BRCA2 protein function with a negative predictive value of 95%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Color Diagnostics, |
RCV000223354 | SCV000911441 | benign | Hereditary cancer-predisposing syndrome | 2016-10-06 | criteria provided, single submitter | clinical testing | |
Mendelics | RCV000112928 | SCV001139001 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2019-05-28 | criteria provided, single submitter | clinical testing | |
University of Washington Department of Laboratory Medicine, |
RCV000223354 | SCV003851439 | likely benign | Hereditary cancer-predisposing syndrome | 2023-03-23 | criteria provided, single submitter | curation | Missense variant in a coldspot region where missense variants are very unlikely to be pathogenic (PMID:31911673). |
Breast Cancer Information Core |
RCV000112928 | SCV000145879 | benign | Breast-ovarian cancer, familial, susceptibility to, 2 | 2010-12-17 | no assertion criteria provided | clinical testing |