Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000166164 | SCV000216938 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-08-29 | criteria provided, single submitter | clinical testing | The p.T515A variant (also known as c.1543A>G), located in coding exon 9 of the BRCA2 gene, results from an A to G substitution at nucleotide position 1543. The threonine at codon 515 is replaced by alanine, an amino acid with similar properties. This amino acid position is poorly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Invitae | RCV000548268 | SCV000635166 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2022-09-17 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt BRCA2 protein function. ClinVar contains an entry for this variant (Variation ID: 186550). This variant has not been reported in the literature in individuals affected with BRCA2-related conditions. This variant is present in population databases (rs749469486, gnomAD 0.007%). This sequence change replaces threonine, which is neutral and polar, with alanine, which is neutral and non-polar, at codon 515 of the BRCA2 protein (p.Thr515Ala). |
Gene |
RCV002254912 | SCV002526257 | uncertain significance | not provided | 2022-05-24 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; Also known as 1771A>G |
University of Washington Department of Laboratory Medicine, |
RCV000166164 | SCV003851466 | likely benign | Hereditary cancer-predisposing syndrome | 2023-03-23 | criteria provided, single submitter | curation | Missense variant in a coldspot region where missense variants are very unlikely to be pathogenic (PMID:31911673). |
All of Us Research Program, |
RCV003995484 | SCV004818691 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2023-03-28 | criteria provided, single submitter | clinical testing |