Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000570541 | SCV000668600 | uncertain significance | Hereditary cancer-predisposing syndrome | 2016-01-21 | criteria provided, single submitter | clinical testing | The p.G578R variant (also known as c.1732G>C), located in coding exon 9 of the BRCA2 gene, results from a G to C substitution at nucleotide position 1732. The glycine at codon 578 is replaced by arginine, an amino acid with dissimilar properties. This variant was not reported in population based cohorts in the following databases: Database of Single Nucleotide Polymorphisms (dbSNP), NHLBI Exome Sequencing Project (ESP), and 1000 Genomes Project. In the ESP, this variant was not observed in 6503 samples (13006 alleles) with coverage at this position. To date, this alteration has been detected with an allele frequency of approximately 0.0004% (greater than 225000 alleles tested) in our clinical cohort. This amino acid position is not well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Color Diagnostics, |
RCV000570541 | SCV001359082 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-06-01 | criteria provided, single submitter | clinical testing | |
Laboratory of Molecular Epidemiology of Birth Defects, |
RCV003153741 | SCV003843666 | likely pathogenic | Ovarian cancer | 2022-01-01 | criteria provided, single submitter | clinical testing | |
University of Washington Department of Laboratory Medicine, |
RCV000570541 | SCV003851600 | likely benign | Hereditary cancer-predisposing syndrome | 2023-03-23 | criteria provided, single submitter | curation | Missense variant in a coldspot region where missense variants are very unlikely to be pathogenic (PMID:31911673). |
Center for Precision Medicine, |
RCV002250660 | SCV002520939 | uncertain significance | Familial cancer of breast | no assertion criteria provided | curation |