Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000700243 | SCV000828991 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2024-10-12 | criteria provided, single submitter | clinical testing | This sequence change replaces lysine, which is basic and polar, with arginine, which is basic and polar, at codon 981 of the BRCA2 protein (p.Lys981Arg). This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with BRCA2-related conditions. ClinVar contains an entry for this variant (Variation ID: 91791). Invitae Evidence Modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) indicates that this missense variant is not expected to disrupt BRCA2 protein function with a negative predictive value of 95%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV002433582 | SCV002747842 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-08-15 | criteria provided, single submitter | clinical testing | The p.K981R variant (also known as c.2942A>G), located in coding exon 10 of the BRCA2 gene, results from an A to G substitution at nucleotide position 2942. The lysine at codon 981 is replaced by arginine, an amino acid with highly similar properties. This amino acid position is poorly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV003155066 | SCV003844669 | uncertain significance | not specified | 2023-02-14 | criteria provided, single submitter | clinical testing | |
University of Washington Department of Laboratory Medicine, |
RCV002433582 | SCV003850258 | likely benign | Hereditary cancer-predisposing syndrome | 2023-03-23 | criteria provided, single submitter | curation | Missense variant in a coldspot region where missense variants are very unlikely to be pathogenic (PMID:31911673). |
Sharing Clinical Reports Project |
RCV000077699 | SCV000109502 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2010-07-27 | no assertion criteria provided | clinical testing |