Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000975297 | SCV001123180 | likely benign | Hereditary breast ovarian cancer syndrome | 2023-03-09 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV001189537 | SCV001356847 | likely benign | Hereditary cancer-predisposing syndrome | 2019-05-01 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV001280618 | SCV001467843 | likely benign | not specified | 2020-12-18 | criteria provided, single submitter | clinical testing | Variant summary: BRCA2 c.317-17T>A alters a non-conserved nucleotide located close to a canonical splice site and therefore could affect mRNA splicing, leading to a significantly altered protein sequence. 4/4 computational tools predict no significant impact on normal splicing. However, these predictions have yet to be confirmed by functional studies. The variant was absent in 249098 control chromosomes. The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.317-17T>A in individuals affected with Hereditary Breast And Ovarian Cancer Syndrome and no experimental evidence demonstrating its impact on protein function have been reported. Two clinical diagnostic laboratories have submitted clinical-significance assessments for this variant to ClinVar after 2014 without evidence for independent evaluation. All laboratories classified the variant as likely benign. Based on the evidence outlined above, and to reflect the emerging consensus, the variant was classified as likely benign. |
Ambry Genetics | RCV001189537 | SCV004915392 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-06-23 | criteria provided, single submitter | clinical testing | The c.317-17T>A intronic alteration consists of a T to A substitution 17 nucleotides before coding exon 3 in the BRCA2 gene. Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |