Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV000587081 | SCV000694693 | uncertain significance | not provided | 2016-04-22 | criteria provided, single submitter | clinical testing | Variant summary: The c.3403T>G variant affects a non-conserved nucleotide, resulting in amino acid change from Tyr to Asp. 3/5 in-silico tools predict this variant to be damaging. This variant is not found in 120770 control chromosomes. The variant of interest has not, to our knowledge, been reported in affected individuals via publications and/or reputable databases/clinical laboratories; nor evaluated for functional impact by in vivo/vitro studies. Because of the absence of clinical information and the lack of functional studies, the variant was classified as a variant of uncertain significance (VUS) until additional information becomes available. |
Ambry Genetics | RCV002456281 | SCV002614977 | uncertain significance | Hereditary cancer-predisposing syndrome | 2017-10-11 | criteria provided, single submitter | clinical testing | The p.Y1135D variant (also known as c.3403T>G), located in coding exon 10 of the BRCA2 gene, results from a T to G substitution at nucleotide position 3403. The tyrosine at codon 1135 is replaced by aspartic acid, an amino acid with highly dissimilar properties. This amino acid position is poorly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
University of Washington Department of Laboratory Medicine, |
RCV002456281 | SCV003851928 | likely benign | Hereditary cancer-predisposing syndrome | 2023-03-23 | criteria provided, single submitter | curation | Missense variant in a coldspot region where missense variants are very unlikely to be pathogenic (PMID:31911673). |