Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001281567 | SCV001468877 | likely pathogenic | Familial cancer of breast | 2019-08-02 | criteria provided, single submitter | clinical testing | The c.5142T>G (p.Tyr1714Ter) variant identified in the BRCA2 gene leads to the premature termination of the protein at amino acid 1714/3419 (coding exon 11/27). This variant is absent from gnomAD and ExAC, suggesting it is not a common benign variant in the populations represented in these databases. Although it is absent from ClinVar, many pathogenic nonsense variants have been reported downstream (https://www.ncbi.nlm.nih.gov/clinvar). To our current knowledge, this variant has not been reported in any affected individuals in the literature. Given its deleterious nature and absence in population databases, the c.5142T>G (p.Tyr1714Ter) variant in the BRCA2 gene is reported here as Likely Pathogenic. |