Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000203759 | SCV000261478 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2023-03-09 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (gnomAD no frequency). This sequence change replaces asparagine, which is neutral and polar, with serine, which is neutral and polar, at codon 2051 of the BRCA2 protein (p.Asn2051Ser). This missense change has been observed in individual(s) with breast and/or ovarian cancer (PMID: 29470806). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt BRCA2 protein function. ClinVar contains an entry for this variant (Variation ID: 91439). |
Ambry Genetics | RCV000222229 | SCV000275243 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-01-03 | criteria provided, single submitter | clinical testing | The p.N2051S variant (also known as c.6152A>G), located in coding exon 10 of the BRCA2 gene, results from an A to G substitution at nucleotide position 6152. The asparagine at codon 2051 is replaced by serine, an amino acid with highly similar properties. This alteration has been reported as a variant of unknown significance in a cohort of 1010 unrelated patients and families from across India with an indication of breast and/or ovarian cancers (Singh J et al. Breast Cancer Res. Treat., 2018 Jul;170:189-196). This amino acid position is poorly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Color Diagnostics, |
RCV000222229 | SCV000906130 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-06-05 | criteria provided, single submitter | clinical testing | |
Mendelics | RCV000076956 | SCV001139138 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2019-05-28 | criteria provided, single submitter | clinical testing | |
University of Washington Department of Laboratory Medicine, |
RCV000222229 | SCV003850980 | likely benign | Hereditary cancer-predisposing syndrome | 2023-03-23 | criteria provided, single submitter | curation | Missense variant in a coldspot region where missense variants are very unlikely to be pathogenic (PMID:31911673). |
All of Us Research Program, |
RCV000076956 | SCV004846711 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2022-12-16 | criteria provided, single submitter | clinical testing | |
Sharing Clinical Reports Project |
RCV000076956 | SCV000108753 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2006-09-01 | no assertion criteria provided | clinical testing |