Total submissions: 9
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV000076987 | SCV000296494 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2016-06-08 | criteria provided, single submitter | clinical testing | |
Counsyl | RCV000076987 | SCV000489623 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2016-10-31 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000562449 | SCV000665933 | likely benign | Hereditary cancer-predisposing syndrome | 2024-10-29 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Mendelics | RCV000076987 | SCV001138976 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2019-05-28 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000709294 | SCV001207986 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2024-12-15 | criteria provided, single submitter | clinical testing | This sequence change replaces aspartic acid, which is acidic and polar, with asparagine, which is neutral and polar, at codon 237 of the BRCA2 protein (p.Asp237Asn). This variant is present in population databases (rs398122575, gnomAD 0.0009%). This variant has not been reported in the literature in individuals affected with BRCA2-related conditions. ClinVar contains an entry for this variant (Variation ID: 91470). Invitae Evidence Modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) indicates that this missense variant is not expected to disrupt BRCA2 protein function with a negative predictive value of 95%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Color Diagnostics, |
RCV000562449 | SCV001736309 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-10-16 | criteria provided, single submitter | clinical testing | This missense variant replaces aspartic acid with asparagine at codon 237 of the BRCA2 protein. Computational prediction suggests that this variant may not impact protein structure and function (internally defined REVEL score threshold <= 0.5, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with BRCA2-related disorders in the literature. This variant has been identified in 1/250352 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Gene |
RCV003317080 | SCV004021522 | uncertain significance | not provided | 2023-07-19 | criteria provided, single submitter | clinical testing | Identified in individual(s) referred for hereditary cancer testing (Li et al., 2020); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Also known as 937G>A; This variant is associated with the following publications: (PMID: 26295337, 32377563, 29884841, 31853058) |
All of Us Research Program, |
RCV004804051 | SCV005424260 | uncertain significance | BRCA2-related cancer predisposition | 2024-09-11 | criteria provided, single submitter | clinical testing | This missense variant replaces aspartic acid with asparagine at codon 237 of the BRCA2 protein. Computational prediction suggests that this variant may not impact protein structure and function (internally defined REVEL score threshold <= 0.5, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with BRCA2-related disorders in the literature. This variant has been identified in 1/250352 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Sharing Clinical Reports Project |
RCV000076987 | SCV000108784 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2009-03-17 | no assertion criteria provided | clinical testing |