Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000464375 | SCV000549772 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2021-06-23 | criteria provided, single submitter | clinical testing | In summary, this variant is a novel missense change with uncertain impact on protein function. It has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C0"). This variant is not present in population databases (ExAC no frequency) and has not been reported in the literature in individuals with a BRCA2-related disease. This sequence change replaces proline with leucine at codon 2804 of the BRCA2 protein (p.Pro2804Leu). The proline residue is highly conserved and there is a moderate physicochemical difference between proline and leucine. |
Color Diagnostics, |
RCV000775812 | SCV000910273 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-05-05 | criteria provided, single submitter | clinical testing | |
Institute for Clinical Genetics, |
RCV003237869 | SCV002010308 | uncertain significance | not provided | 2021-11-03 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000775812 | SCV005548652 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-07-11 | criteria provided, single submitter | clinical testing | The p.P2804L variant (also known as c.8411C>T), located in coding exon 18 of the BRCA2 gene, results from a C to T substitution at nucleotide position 8411. The proline at codon 2804 is replaced by leucine, an amino acid with similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |