Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000476089 | SCV000549537 | uncertain significance | Hereditary breast ovarian cancer syndrome | 2024-07-16 | criteria provided, single submitter | clinical testing | This variant, c.8418_8420del, results in the deletion of 1 amino acid(s) of the BRCA2 protein (p.Ser2807del), but otherwise preserves the integrity of the reading frame. This variant is not present in population databases (gnomAD no frequency). This variant has been observed in individual(s) with breast and/or ovarian cancer (PMID: 35918668). ClinVar contains an entry for this variant (Variation ID: 409445). Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV001017727 | SCV001178853 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-06-12 | criteria provided, single submitter | clinical testing | The c.8418_8420delATC variant (also known as p.S2807del) is located in coding exon 18 of the BRCA2 gene. This variant results from an in-frame ATC deletion at nucleotide positions 8418 to 8420. This results in the in-frame deletion of a serine at codon 2807. This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive (Choi Y et al. PLoS ONE. 2012; 7(10):e46688). Based on the available evidence, the clinical significance of this variant remains unclear. |
Centre for Mendelian Genomics, |
RCV001197319 | SCV001367998 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2019-03-07 | criteria provided, single submitter | clinical testing | This variant was classified as: Uncertain significance. The available evidence on this variant's pathogenicity is insufficient or conflicting. The following ACMG criteria were applied in classifying this variant: PM2,PP4. |
Gene |
RCV004760509 | SCV005373262 | uncertain significance | not provided | 2023-08-04 | criteria provided, single submitter | clinical testing | In-frame deletion of 1 amino acid in a non-repeat region; In silico analysis supports a deleterious effect on protein structure/function; Located in the critical DNA binding domain (Yang et al., 2002); Not observed at significant frequency in large population cohorts (gnomAD); Observed in a patient with breast or ovarian cancer (Zhang et al., 2022); Also known as 8646_8648del; This variant is associated with the following publications: (PMID: 35918668, 12228710) |
Center for Precision Medicine, |
RCV002250630 | SCV002520842 | uncertain significance | Familial cancer of breast | no assertion criteria provided | literature only |