Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV005052412 | SCV005685639 | likely pathogenic | not provided | 2024-07-13 | criteria provided, single submitter | clinical testing | RNA studies demonstrated aberrant splicing, producing multiple transcripts that are predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease (PMID: 22632462); Not observed at significant frequency in large population cohorts (gnomAD); Also known as 8716-2A>G; This variant is associated with the following publications: (PMID: 23893897, 29922827, 22632462) |