Total submissions: 13
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001083702 | SCV000073572 | likely benign | Hereditary breast ovarian cancer syndrome | 2025-01-21 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000589428 | SCV000210550 | likely benign | not provided | 2021-02-03 | criteria provided, single submitter | clinical testing | This variant is associated with the following publications: (PMID: 27225819, 24323938, 28263838, 25348012, 27062684, 24817641, 29061375, 26689913, 21671020, 23328489, 31131967) |
Ambry Genetics | RCV000163478 | SCV000214033 | likely benign | Hereditary cancer-predisposing syndrome | 2019-04-17 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Counsyl | RCV000077446 | SCV000488225 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2016-01-27 | criteria provided, single submitter | clinical testing | |
ARUP Laboratories, |
RCV000045559 | SCV000602869 | likely benign | not specified | 2017-02-27 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000163478 | SCV000683984 | likely benign | Hereditary cancer-predisposing syndrome | 2015-02-19 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV000045559 | SCV000695164 | likely benign | not specified | 2024-11-11 | criteria provided, single submitter | clinical testing | Variant summary: BRCA2 c.856T>C (p.Ser286Pro) results in a non-conservative amino acid change in the encoded protein sequence. Four of five in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 2.1e-05 in 240246 control chromosomes (gnomAD). The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. c.856T>C has been reported in the literature in individuals affected with Hereditary Breast and Ovarian Cancer (example: Balia 2011, Azzollini 2016, Solmaz_2020, Dorling_2021, Patruno_2021). These reports do not provide unequivocal conclusions about association of the variant with Hereditary Breast And Ovarian Cancer Syndrome. Co-occurrences with pathogenic variants have been reported (BRCA1 c.5266dupC, p.Gln1756ProfsX74; BIC database) and have been observed internally (BRCA1 c.1044T>A, p.Cys348X), providing supporting evidence for a benign role. Several publications reported experimental evidence evaluating an impact on protein function (Balia 2011, Guidugli 2013, Spugnesi 2013). These results showed no damaging effect for this variant. The following publications have been ascertained in the context of this evaluation (PMID: 27062684, 21671020, 29061375, 33471991, 24323938, 26689913, 34572941, 31954625, 23328489, 28263838). ClinVar contains an entry for this variant (Variation ID: 52622). Based on the evidence outlined above, the variant was classified as likely benign. |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV000589428 | SCV001470253 | likely benign | not provided | 2023-05-15 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000163478 | SCV002531959 | likely benign | Hereditary cancer-predisposing syndrome | 2021-02-22 | criteria provided, single submitter | curation | |
University of Washington Department of Laboratory Medicine, |
RCV000163478 | SCV003848088 | likely benign | Hereditary cancer-predisposing syndrome | 2023-03-23 | criteria provided, single submitter | curation | Missense variant in a coldspot region where missense variants are very unlikely to be pathogenic (PMID:31911673). |
Sharing Clinical Reports Project |
RCV000077446 | SCV000109244 | likely benign | Breast-ovarian cancer, familial, susceptibility to, 2 | 2013-03-04 | no assertion criteria provided | clinical testing | |
Breast Cancer Information Core |
RCV000077446 | SCV000145780 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2002-06-20 | no assertion criteria provided | clinical testing | |
BRCAlab, |
RCV000077446 | SCV004244081 | likely benign | Breast-ovarian cancer, familial, susceptibility to, 2 | 2020-03-02 | no assertion criteria provided | clinical testing |