Total submissions: 11
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000218620 | SCV000273382 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-03-14 | criteria provided, single submitter | clinical testing | The p.S3131P variant (also known as c.9391T>C), located in coding exon 24 of the BRCA2 gene, results from a T to C substitution at nucleotide position 9391. The serine at codon 3131 is replaced by proline, an amino acid with similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV000506488 | SCV000600860 | uncertain significance | not specified | 2017-04-08 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000218620 | SCV000906701 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-01-05 | criteria provided, single submitter | clinical testing | This missense variant replaces serine with proline at codon 3131 of the BRCA2 protein. Computational prediction is inconclusive regarding the impact of this variant on protein structure and function (internally defined REVEL score threshold 0.5 < inconclusive < 0.7, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with hereditary cancer in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Labcorp Genetics |
RCV001219085 | SCV001391006 | likely benign | Hereditary breast ovarian cancer syndrome | 2025-01-07 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000218620 | SCV002532028 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-08-03 | criteria provided, single submitter | curation | |
Gene |
RCV002466422 | SCV002762556 | uncertain significance | not provided | 2022-06-07 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; Also known as 9619T>C; This variant is associated with the following publications: (PMID: 12228710) |
All of Us Research Program, |
RCV000077041 | SCV004846167 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2023-07-07 | criteria provided, single submitter | clinical testing | This missense variant replaces serine with proline at codon 3131 of the BRCA2 protein. Computational prediction is inconclusive regarding the impact of this variant on protein structure and function (internally defined REVEL score threshold 0.5 < inconclusive < 0.7, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with hereditary cancer in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Baylor Genetics | RCV004566939 | SCV005058986 | uncertain significance | Familial cancer of breast | 2024-03-18 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV005007989 | SCV005633997 | uncertain significance | Familial cancer of breast; Breast-ovarian cancer, familial, susceptibility to, 2; Fanconi anemia complementation group D1; Medulloblastoma; Wilms tumor 1; Pancreatic cancer, susceptibility to, 2; Glioma susceptibility 3; Familial prostate cancer | 2024-02-02 | criteria provided, single submitter | clinical testing | |
Sharing Clinical Reports Project |
RCV000077041 | SCV000108838 | uncertain significance | Breast-ovarian cancer, familial, susceptibility to, 2 | 2012-10-03 | no assertion criteria provided | clinical testing | |
Prevention |
RCV004732651 | SCV005355335 | uncertain significance | BRCA2-related disorder | 2024-09-02 | no assertion criteria provided | clinical testing | The BRCA2 c.9391T>C variant is predicted to result in the amino acid substitution p.Ser3131Pro. This variant has been reported in both individuals with breast cancer and in unaffected individuals (Breast Cancer Association Consortium et al 2021. PubMed ID: 33471991). This variant has an interpretation of uncertain significance in ClinVar (https://www.ncbi.nlm.nih.gov/clinvar/variation/91524/). At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |