Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000370228 | SCV000345118 | uncertain significance | not provided | 2016-08-16 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003517180 | SCV004296937 | pathogenic | Autosomal recessive limb-girdle muscular dystrophy type 2A | 2024-04-25 | criteria provided, single submitter | clinical testing | This sequence change replaces phenylalanine, which is neutral and non-polar, with serine, which is neutral and polar, at codon 569 of the CAPN3 protein (p.Phe569Ser). This variant is not present in population databases (gnomAD no frequency). This missense change has been observed in individual(s) with autosomal recessive limb-girdle muscular dystrophy (PMID: 16141003, 21204801, 32403337, 32896923; Invitae). ClinVar contains an entry for this variant (Variation ID: 290547). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt CAPN3 protein function with a positive predictive value of 80%. For these reasons, this variant has been classified as Pathogenic. |
Fulgent Genetics, |
RCV005008262 | SCV005637796 | likely pathogenic | Autosomal recessive limb-girdle muscular dystrophy type 2A; Muscular dystrophy, limb-girdle, autosomal dominant 4 | 2024-03-01 | criteria provided, single submitter | clinical testing |