Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003494764 | SCV004297409 | pathogenic | HYPERHOMOCYSTEINEMIA, THROMBOTIC, CBS-RELATED | 2023-05-05 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant is also known as 753delG (V252fsX268). This premature translational stop signal has been observed in individual(s) with homocystinuria (PMID: 20051935). This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Val252Trpfs*17) in the CBS gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CBS are known to be pathogenic (PMID: 10338090, 12124992). |