Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000160404 | SCV000210936 | pathogenic | Hereditary cancer-predisposing syndrome | 2013-10-30 | criteria provided, single submitter | clinical testing | The CDKN2A c.206_229delinsCAG mutation causes an in-frame deletion of nine amino acids starting with Glutamic Acid 69 and ending with Threonine 77 and the insertion of two Alanine residues, denoted p.Glu69_Thr77delinsAlaAla. This in-frame deletion and insertion is expected to disrupt the protein structure and/or function. Although this mutation has not been previously reported to our knowledge, its presence is consistent with a risk to develop features of familial cutaneous malignant melanoma. This variant has been observed to be inherited. The variant is found in CDKN2A panel(s). |