Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV001016352 | SCV001177300 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-03-20 | criteria provided, single submitter | clinical testing | The p.M9R variant (also known as c.26T>G), located in coding exon 1 of the CDKN2A gene, results from a T to G substitution at nucleotide position 26. The methionine at codon 9 is replaced by arginine, an amino acid with similar properties. This amino acid position is not conserved on limited sequence alignment. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this alteration remains unclear. |
Labcorp Genetics |
RCV001040669 | SCV001204256 | uncertain significance | Familial melanoma | 2025-01-06 | criteria provided, single submitter | clinical testing | This sequence change replaces methionine, which is neutral and non-polar, with arginine, which is basic and polar, at codon 9 of the CDKN2A (p16INK4a) protein (p.Met9Arg). This variant is present in population databases (rs145445140, gnomAD 0.003%). This variant has not been reported in the literature in individuals affected with CDKN2A (p16INK4a)-related conditions. ClinVar contains an entry for this variant (Variation ID: 821690). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Color Diagnostics, |
RCV001016352 | SCV001350133 | uncertain significance | Hereditary cancer-predisposing syndrome | 2019-01-31 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV005047208 | SCV005680460 | uncertain significance | Melanoma-pancreatic cancer syndrome; Melanoma, cutaneous malignant, susceptibility to, 2; Melanoma and neural system tumor syndrome | 2024-05-21 | criteria provided, single submitter | clinical testing |