Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000218034 | SCV000277887 | pathogenic | Hereditary cancer-predisposing syndrome | 2017-05-01 | criteria provided, single submitter | clinical testing | The c.340_343dupCCCG pathogenic mutation, located in coding exon 2 of the CDKN2A gene, results from a duplication of CCCG at nucleotide position 340, causing a translational frameshift with a predicted alternate stop codon (p.V115Afs*6). This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |