Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Department Of Human Genetics, |
RCV004527495 | SCV005038729 | likely pathogenic | Congenital myotonia, autosomal recessive form; Congenital myotonia, autosomal dominant form | criteria provided, single submitter | research | The c.1255A>T (p.(Met419Leu)) variant was found in a heterozygous state in 1 Slovak patient with Myotonia congenita. No other pathogenic or likely pathogenic variants were found in this individual, whose alternative diagnosis was also Myotonic Dystrophy. The c.1255A>T variant is not listed in the publicly available HGMD database (CM940286) and neither in dbSNP nor GnomAD Exomes databases. |