Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV000191071 | SCV000245463 | likely pathogenic | Osteogenesis imperfecta type I | 2014-02-04 | criteria provided, single submitter | clinical testing | Likely pathogenicity based on finding it once in our laboratory de novo in a 22-year-old female with IUGR, hearing loss, large fontanel, blue sclerae, large amount of soft tissue in neck, abnormal shaped ears, short stature, strabismic amblyopia with anisometropia, thin membranous bones, osteoporosis, thin skin |