Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002281710 | SCV002571672 | pathogenic | not provided | 2022-09-12 | criteria provided, single submitter | clinical testing | Affects a glycine residue in a Gly-X-Y motif in the triple helical region of the COL1A2 gene, where the majority of pathogenic missense variants occur; Not observed in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 2914942) |
OMIM | RCV000018779 | SCV000039062 | pathogenic | Osteogenesis imperfecta, perinatal lethal | 1989-02-15 | no assertion criteria provided | literature only |