Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002284361 | SCV002574591 | likely pathogenic | not provided | 2022-02-23 | criteria provided, single submitter | clinical testing | This variant is demonstrated to affect the canonical splice donor site and result in a null allele in a gene for which loss-of-function is a known mechanism of disease (Leistritz et al., 2011); Identified in an individual with either a personal or family history of a major arterial event, but specific clinical information was not provided (Leistritz et al., 2011); Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 25525159, 24922459, 21637106) |
Collagen Diagnostic Laboratory, |
RCV000087347 | SCV000120227 | pathogenic | Ehlers-Danlos syndrome, type 4 | no assertion criteria provided | clinical testing |