Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Juno Genomics, |
RCV004795783 | SCV005418012 | uncertain significance | Autosomal dominant Alport syndrome; Autosomal recessive Alport syndrome; Hematuria, benign familial, 1 | criteria provided, single submitter | clinical testing | PM2_Supporting+PP3+PP4+PM6 | |
Laboratory of Prof. |
RCV004821345 | SCV005442593 | uncertain significance | Autosomal dominant Alport syndrome | 2024-12-25 | criteria provided, single submitter | research | The COL4A3 c.1805G>A:p.(Gly602Asp) heterozygous variant is predicted deleterious and not found in gnomAD. It was detected in an individual with moderate-severe HL. |