Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV001442689 | SCV001645642 | likely benign | not provided | 2024-01-29 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV001442689 | SCV003833708 | uncertain significance | not provided | 2022-08-01 | criteria provided, single submitter | clinical testing | |
Johns Hopkins Genomics, |
RCV003485717 | SCV004239056 | uncertain significance | Benign familial hematuria | 2023-10-24 | criteria provided, single submitter | clinical testing | COL4A4 c.2629C>T in the heterozygous state has been reported as a de novo occurrence in a patient with end stage renal disease and hearing loss who also had muscular atrophy and intellectual disability. This missense variant (rs55948916) has also been reported in ClinVar (Variation ID 1114838), and is rare (<0.1%) in a large population dataset (gnomAD v3.1.2: 39/152016 total alleles; 0.03%; no homozygotes). Two bioinformatic tools queried predict that this substitution would be tolerated, and the arginine residue at this position is evolutionarily conserved across some of the species assessed. We consider the clinical significance of c.2629C>T in COL4A4 to be uncertain at this time. |