Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Diagnostics Laboratory, |
RCV000760147 | SCV000889956 | pathogenic | Ehlers-Danlos syndrome, classic type | 2016-09-08 | criteria provided, single submitter | clinical testing | |
Neuberg Centre For Genomic Medicine, |
RCV004555594 | SCV005044828 | likely pathogenic | Ehlers-Danlos syndrome, classic type, 1 | criteria provided, single submitter | clinical testing | The invariant splice donor c.4338+1G>A in COL5A1 gene has been submitted to ClinVar as a Pathogenic, but no details are available for independent assessment. The c.4338+1G>A variant is novel not in any individuals in 1000 Genomes and gnomAD Exomes. Functional studies are required to prove the pathogenicity for the variant. For these reasons, this variant has been classified as Likely Pathogenic. |