Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002240305 | SCV001209609 | benign | Ehlers-Danlos syndrome, classic type, 1 | 2024-11-06 | criteria provided, single submitter | clinical testing | |
Mayo Clinic Laboratories, |
RCV001509380 | SCV001716056 | uncertain significance | not provided | 2023-05-02 | criteria provided, single submitter | clinical testing | BS1, PP3 |
Gene |
RCV001509380 | SCV002007210 | uncertain significance | not provided | 2023-03-02 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge; In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Not located in the triple helical region, where the majority of pathogenic missense variants occur (Symoens et al., 2012; HGMD); This variant is associated with the following publications: (PMID: 22696272) |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV005408661 | SCV006071805 | uncertain significance | not specified | 2025-03-28 | criteria provided, single submitter | clinical testing | Variant summary: COL5A1 c.5194C>T (p.Arg1732Trp) results in a non-conservative amino acid change in the encoded protein sequence. Five of five in-silico tools predict a damaging effect of the variant on protein function. The variant allele was found at a frequency of 2.8e-05 in 249936 control chromosomes (gnomAD). The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.5194C>T in individuals affected with Ehlers-Danlos syndrome, classic type, Ehlers-Danlos syndrome, classic type, 1 and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 843180). Based on the evidence outlined above, the variant was classified as uncertain significance. |