Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV001808912 | SCV002059165 | uncertain significance | Epidermolysis bullosa pruriginosa | 2022-01-03 | criteria provided, single submitter | clinical testing | A different missense change at the same codon has been reported as pathogenic/likely pathogenic with strong evidence (ClinVar ID: VCV000279789, PMID:23397949, PM5_M). It is observed at an extremely low frequency in the gnomAD v2.1.1 dataset (total allele frequency: 0.000000, PM2_M). In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.885, PP3_P). Therefore, this variant is classified as uncertain significance according to the recommendation of ACMG/AMP guideline. |