Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Biomedical Innovation Departament, |
RCV001352697 | SCV001547275 | pathogenic | Epidermolysis bullosa dystrophica | 2008-11-04 | criteria provided, single submitter | research | |
Laboratorio de Genetica e Diagnostico Molecular, |
RCV002245973 | SCV002512596 | pathogenic | Recessive dystrophic epidermolysis bullosa; Generalized dominant dystrophic epidermolysis bullosa | 2022-02-09 | criteria provided, single submitter | clinical testing | ACMG classification criteria: PVS1 very strong, PS4 moderate, PM2 moderate, PM3 strong, PP1 supporting, PP1 |
Fulgent Genetics, |
RCV002476621 | SCV002777031 | pathogenic | Recessive dystrophic epidermolysis bullosa; Pretibial dystrophic epidermolysis bullosa; Dominant dystrophic epidermolysis bullosa with absence of skin; Transient bullous dermolysis of the newborn; Epidermolysis bullosa pruriginosa; Nonsyndromic congenital nail disorder 8; Generalized dominant dystrophic epidermolysis bullosa | 2021-12-15 | criteria provided, single submitter | clinical testing |