Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002283712 | SCV002572712 | likely pathogenic | Recessive dystrophic epidermolysis bullosa | 2022-09-01 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. In silico tool predictions suggest damaging effect of the variant on gene or gene product (REVEL: 0.97; 3Cnet: 0.89). Same nucleotide change resulting in same amino acid change has been previously reported to be associated with COL7A1 -related disorder (PMID: 29512197). The variant has been reported to be in trans with a pathogenic variant as either compound heterozygous or homozygous in at least one similarly affected unrelated individual (PMID: 29512197). Therefore, this variant is classified as Likely pathogenic according to the recommendation of ACMG/AMP guideline. |