Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003340722 | SCV004047393 | uncertain significance | Generalized dominant dystrophic epidermolysis bullosa | criteria provided, single submitter | clinical testing | The missense variant c.811G>C (p.Gly271Arg) in COL7A1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Gly271Arg variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. The amino acid Gly at position 271 is changed to a Arg changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Gly271Arg in COL7A1 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |