Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000806853 | SCV000946872 | likely pathogenic | not provided | 2023-09-10 | criteria provided, single submitter | clinical testing | In summary, the currently available evidence indicates that the variant is pathogenic, but additional data are needed to prove that conclusively. Therefore, this variant has been classified as Likely Pathogenic. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. ClinVar contains an entry for this variant (Variation ID: 651482). Disruption of the initiator codon has been observed in individual(s) with 17-alpha-hydroxylase deficiency (PMID: 9855540, 14715827). In at least one individual the data is consistent with being in trans (on the opposite chromosome) from a pathogenic variant. This variant is not present in population databases (gnomAD no frequency). This sequence change affects the initiator methionine of the CYP17A1 mRNA. The next in-frame methionine is located at codon 49. |
Fulgent Genetics, |
RCV001830758 | SCV002790868 | likely pathogenic | Deficiency of steroid 17-alpha-monooxygenase | 2022-03-28 | criteria provided, single submitter | clinical testing | |
Natera, |
RCV001830758 | SCV002085627 | likely pathogenic | Deficiency of steroid 17-alpha-monooxygenase | 2021-01-26 | no assertion criteria provided | clinical testing |