Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004587970 | SCV005075774 | uncertain significance | not specified | 2024-04-03 | criteria provided, single submitter | clinical testing | Variant summary: CYP19A1 c.1124G>T (p.Arg375Leu) results in a non-conservative amino acid change in the encoded protein sequence. Five of five in-silico tools predict a damaging effect of the variant on protein function. The variant was absent in 251176 control chromosomes (gnomAD). To our knowledge, no occurrence of c.1124G>T in individuals affected with Aromatase deficiency and no experimental evidence demonstrating its impact on protein function have been reported. A different missense change affecting this amino acid has been determined to be pathogenic, suggesting this may be a functionally important residue. No submitters have cited clinical-significance assessments for this variant to ClinVar. Based on the evidence outlined above, the variant was classified as VUS-possibly pathogenic. |