Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002251048 | SCV002521413 | likely pathogenic | Glaucoma 3A | 2022-05-22 | criteria provided, single submitter | clinical testing | The variant is observed at an extremely low frequency in the gnomAD v2.1.1 dataset (total allele frequency: <0.001%). Frameshift: predicted to result in a loss or disruption of normal protein function through protein truncation. The predicted truncated protein may be shortened by more than 10%. The variant has been reported to be associated with CYP1B1- related disorder (PMID: 27508083). Therefore, this variant is classified as likely pathogenic according to the recommendation of ACMG/AMP guideline. |
Gene |
RCV003238892 | SCV003936477 | pathogenic | not provided | 2023-06-29 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation, as the last 102 amino acids are replaced with 14 different amino acids, and other loss-of-function variants have been reported downstream in the Human Gene Mutation Database (HGMD); Not observed at a significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 27777502, 27508083, 30820150, 35085548) |