Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000409426 | SCV000485577 | likely pathogenic | Dihydropyrimidine dehydrogenase deficiency | 2016-01-07 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV000409426 | SCV001467803 | likely pathogenic | Dihydropyrimidine dehydrogenase deficiency | 2020-12-02 | criteria provided, single submitter | clinical testing | Variant summary: DPYD c.1863G>A (p.Trp621X) results in a premature termination codon, predicted to cause a truncation of the encoded protein or absence of the protein due to nonsense mediated decay, which are commonly known mechanisms for disease. The variant allele was found at a frequency of 1.2e-05 in 251336 control chromosomes. c.1863G>A has been reported in the literature as a de-novo mutation in an individual affected with schizophrenia (e.g. Xu_2012). The variant was also found in a cancer patient who experienced toxicity following treatment with fluoropyrimidine (e.g. Yokoi_2020). These data do not allow any conclusion about variant significance. To our knowledge, no experimental evidence demonstrating an impact on protein function has been reported. One clinical diagnostic laboratory has submitted clinical-significance assessments for this variant to ClinVar after 2014 without evidence for independent evaluation and cited the variant as likely pathogenic. Based on the evidence outlined above, the variant was classified as likely pathogenic. |
Gene |
RCV003236797 | SCV003935607 | likely pathogenic | not provided | 2023-06-21 | criteria provided, single submitter | clinical testing | De novo variant in a patient with schizoaffective disorder, however, it is unclear if this patient had variants identified in other genes, and additional research is needed to explore this possible association (Xu et al., 2011); Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 23042115, 31589614, 25420024) |
Genome- |
RCV000409426 | SCV004049536 | likely pathogenic | Dihydropyrimidine dehydrogenase deficiency | 2023-04-11 | criteria provided, single submitter | clinical testing |