Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001853038 | SCV002238780 | pathogenic | not provided | 2024-03-13 | criteria provided, single submitter | clinical testing | This sequence change affects an acceptor splice site in intron 5 of the SLC26A3 gene. It is expected to disrupt RNA splicing. Variants that disrupt the donor or acceptor splice site typically lead to a loss of protein function (PMID: 16199547), and loss-of-function variants in SLC26A3 are known to be pathogenic (PMID: 9718329, 21394828). This variant is present in population databases (rs386833485, gnomAD 0.002%). Disruption of this splice site has been observed in individuals with congenital chloride diarrhea (PMID: 9718329). This variant is also known as IVS5-1G>T. ClinVar contains an entry for this variant (Variation ID: 56004). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. For these reasons, this variant has been classified as Pathogenic. |
Genetics and Molecular Pathology, |
RCV000049413 | SCV002761408 | pathogenic | Congenital secretory diarrhea, chloride type | 2022-07-05 | criteria provided, single submitter | clinical testing | |
Juha Muilu Group; Institute for Molecular Medicine Finland |
RCV000049413 | SCV000081846 | probable-pathogenic | Congenital secretory diarrhea, chloride type | no assertion criteria provided | not provided | Converted during submission to Likely pathogenic. |