Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000409678 | SCV000487664 | likely pathogenic | Diastrophic dysplasia | 2016-07-18 | criteria provided, single submitter | clinical testing | |
Counsyl | RCV000410828 | SCV000487665 | likely pathogenic | Multiple epiphyseal dysplasia type 4 | 2016-07-18 | criteria provided, single submitter | clinical testing | |
Counsyl | RCV000412349 | SCV000487666 | likely pathogenic | Atelosteogenesis type II | 2016-07-18 | criteria provided, single submitter | clinical testing | |
Counsyl | RCV000409864 | SCV000487667 | likely pathogenic | Achondrogenesis, type IB | 2016-07-18 | criteria provided, single submitter | clinical testing | |
Invitae | RCV001850977 | SCV002235510 | pathogenic | Achondrogenesis, type IB; Atelosteogenesis type II; Multiple epiphyseal dysplasia type 4; Diastrophic dysplasia | 2023-12-19 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Ile514Metfs*14) in the SLC26A2 gene. While this is not anticipated to result in nonsense mediated decay, it is expected to disrupt the last 226 amino acid(s) of the SLC26A2 protein. This variant is present in population databases (no rsID available, gnomAD 0.0009%). This variant has not been reported in the literature in individuals affected with SLC26A2-related conditions. ClinVar contains an entry for this variant (Variation ID: 371758). This variant disrupts a region of the SLC26A2 protein in which other variant(s) (p.Glu703Glyfs*9) have been determined to be pathogenic (Invitae). This suggests that this is a clinically significant region of the protein, and that variants that disrupt it are likely to be disease-causing. For these reasons, this variant has been classified as Pathogenic. |
Baylor Genetics | RCV000409864 | SCV004201750 | likely pathogenic | Achondrogenesis, type IB | 2024-02-20 | criteria provided, single submitter | clinical testing |