Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV003389291 | SCV004101302 | likely pathogenic | Emery-Dreifuss muscular dystrophy 1, X-linked | 2023-08-15 | criteria provided, single submitter | clinical testing | The EMD c.441C>A p.(Cys147Ter) nonsense variant results in the loss of normal protein function through either protein truncation or nonsense-mediated mRNA decay. This variant is not observed in version 2.1.1 or version 3.1.2 of the Genome Aggregation Database. Based on the available evidence, the c.441C>A p.(Cys147Ter) variant is classified as likely pathogenic for Emery-Dreifuss muscular dystrophy. |