Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003492838 | SCV003831905 | uncertain significance | Emery-Dreifuss muscular dystrophy 1, X-linked | 2019-11-20 | criteria provided, single submitter | clinical testing | |
3billion | RCV003147047 | SCV003841655 | uncertain significance | X-linked Emery-Dreifuss muscular dystrophy | 2023-02-23 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. Protein truncation variants are a common disease-causing mechanism. The variant is shared with a similarly affected family member. Therefore, this variant is classified as VUS according to the recommendation of ACMG/AMP guideline. |