Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000169501 | SCV000220963 | likely pathogenic | Hereditary factor XI deficiency disease | 2014-12-18 | criteria provided, single submitter | literature only | |
Labcorp Genetics |
RCV001248521 | SCV001422015 | pathogenic | not provided | 2023-04-16 | criteria provided, single submitter | clinical testing | This variant is present in population databases (rs747702749, gnomAD 0.006%). This premature translational stop signal has been observed in individual(s) with Factor XI deficiency (PMID: 16787881, 21668437). This variant is also known as Gln226X. ClinVar contains an entry for this variant (Variation ID: 189094). For these reasons, this variant has been classified as Pathogenic. This sequence change creates a premature translational stop signal (p.Gln244*) in the F11 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in F11 are known to be pathogenic (PMID: 23929304). |