Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003596843 | SCV004293801 | pathogenic | Congenital factor V deficiency | 2023-02-16 | criteria provided, single submitter | clinical testing | This variant is also known as Frameshift, stop at 900. For these reasons, this variant has been classified as Pathogenic. This premature translational stop signal has been observed in individual(s) with Factor V deficiency (PMID: 11167768). This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Thr915Trpfs*14) in the F5 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in F5 are known to be pathogenic (PMID: 30924984). |