Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
NIHR Bioresource Rare Diseases, |
RCV000851824 | SCV000899808 | uncertain significance | Abnormal bleeding | 2019-02-01 | criteria provided, single submitter | research | |
Labcorp Genetics |
RCV003596550 | SCV004274017 | uncertain significance | Congenital factor V deficiency | 2024-01-16 | criteria provided, single submitter | clinical testing | This sequence change replaces methionine, which is neutral and non-polar, with threonine, which is neutral and polar, at codon 1874 of the F5 protein (p.Met1874Thr). This variant is present in population databases (rs377129476, gnomAD 0.02%). This missense change has been observed in individual(s) with unexplained bleeding (PMID: 31064749). ClinVar contains an entry for this variant (Variation ID: 627095). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt F5 protein function with a negative predictive value of 95%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |