Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics Munich, |
RCV000578443 | SCV000680222 | likely pathogenic | Hereditary factor VIII deficiency disease | 2017-12-18 | criteria provided, single submitter | clinical testing | |
Neuberg Centre For Genomic Medicine, |
RCV000578443 | SCV004100481 | uncertain significance | Hereditary factor VIII deficiency disease | criteria provided, single submitter | clinical testing | The missense variant p.N583S in F8 (NM_000132.4) has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. It has been submitted to ClinVar as Likely Pathogenic but no details are available for independent assessment. The p.N583S variant is observed in 3/19,080 (0.0157%) alleles from individuals of South Asian background in gnomAD Exomes and is novel (not in any individuals) in 1000 Genomes. secondary protein structure as these residues share similar properties. For these reasons, this variant has been classified as Uncertain Significance. |