Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV001002494 | SCV001160448 | pathogenic | Hereditary factor VIII deficiency disease | 2019-04-25 | criteria provided, single submitter | clinical testing | The F8 c.5301C>A; p.Tyr1767Ter variant is reported in the literature in at least one individual affected with severe hemophilia A (Bogdanova 2005). This variant is also absent from general population databases (Exome Variant Server, Genome Aggregation Database), indicating it is not a common polymorphism. This variant induces an early termination codon and is predicted to result in a truncated protein or mRNA subject to nonsense-mediated decay. Based on available information, this variant is considered to be pathogenic. References: Bogdanova N et al. Spectrum of molecular defects and mutation detection rate in patients with severe hemophilia A. Hum Mutat. 2005 Sep;26(3):249-54. |