Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
ARUP Laboratories, |
RCV000756109 | SCV000883827 | pathogenic | not provided | 2017-12-06 | criteria provided, single submitter | clinical testing | The F8 c.5879G>A; p.Arg1960Gln variant (rs28937294) has been reported in several individuals with mild hemophilia A (see F8 database link and references therein) and in the ClinVar database (Variation ID: 10110). This variant is absent from general population databases (1000 Genomes Project, Exome Variant Server, Genome Aggregation Database). The arginine at codon 1960 is well conserved and computational algorithms (SIFT, PolyPhen2, MutationTaster) predict this variant to be deleterious. Based on the above information, this variant is considered pathogenic. References: Link to p.Arg1960Gln in F8 Variant Database: http://www.factorviii-db.org/newstructure.php?aa_first=Arg&mut_id=1423&aa_last=Gln&variable=1423&hash=a3c7518bdeb6cb1e707ce33f837f89b4 |
Genetics and Molecular Pathology, |
RCV000010822 | SCV002556782 | likely pathogenic | Hereditary factor VIII deficiency disease | 2021-07-08 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000010822 | SCV000031049 | pathogenic | Hereditary factor VIII deficiency disease | 1990-05-01 | no assertion criteria provided | literature only |