Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003764554 | SCV004571521 | likely pathogenic | Hereditary factor IX deficiency disease; Thrombophilia, X-linked, due to factor 9 defect | 2023-01-30 | criteria provided, single submitter | clinical testing | Studies have shown that this variant does not significantly alter or has an unclear effect on F9 gene expression (PMID: 31395865). This variant occurs in a non-coding region of the F9 gene. It does not change the encoded amino acid sequence of the F9 protein. This variant is not present in population databases (gnomAD no frequency). This variant has been observed in individuals with hemophilia B (PMID: 2917196, 17014892). This variant is also known as A13G. ClinVar contains an entry for this variant (Variation ID: 10646). In summary, the currently available evidence indicates that the variant is pathogenic, but additional data are needed to prove that conclusively. Therefore, this variant has been classified as Likely Pathogenic. |
Mayo Clinic Laboratories, |
RCV004791217 | SCV005413440 | likely pathogenic | not provided | 2024-07-11 | criteria provided, single submitter | clinical testing | PP4, PM1, PM2, PS4_moderate |
OMIM | RCV000011392 | SCV000031624 | pathogenic | Hemophilia B leyden | 1989-02-15 | no assertion criteria provided | literature only |